Important

It is possible that the main title of the report Prune Belly Syndrome is not the name you expected. Please check the synonyms listing to find the alternate name(s) and disorder subdivision(s) covered by this report.

Synonyms

• Abdominal Muscle Deficiency Syndrome
• Congenital Absence of the Abdominal Muscles
• Eagle-Barrett Syndrome
• Obrinsky Syndrome

Disorder Subdivisions

• None

General Discussion

Prune-Belly Syndrome, also known as Eagle-Barrett Syndrome, is a rare disorder characterized by partial or complete absence of the stomach (abdominal) muscles, failure of both testes to descend into the scrotum (bilateral cryptorchidism), and/or urinary tract malformations, such as abnormal widening (dilation) of the tubes that bring urine to the bladder (ureters), accumulation of urine in the ureters (hydroureter) and the kidneys (hydronephrosis), and/or backflow of urine from the bladder into the ureters (vesicoureteral reflux). Complications associated with Prune-Belly Syndrome may include underdevelopment of the lungs (pulmonary hypoplasia) and/or chronic renal failure. The exact cause of Prune-Belly Syndrome is not known.

Resources

Outside Pakistan:

National Prune Belly Syndrome Network
100 UCLA Medical Plaza
Suite 690
Los Angeles, CA 90095
Tel: (310)825-6865
Fax: (310)794-9962

NIH/National Digestive Diseases Information Clearinghouse

2 Information Way
Bethesda, MD 20892-3570
Tel: (301)654-3810
Fax: (301)907-8906
Tel: (800)891-5389
Email: nddic@info.niddk.nih.gov
Internet: http://www.niddk.nih.gov